Disease manifestation | anti-PM/Scl-75-positive (n = 29) | anti-PM/Scl-75-negative (n = 251) | P value | Sensitivity, percentagea | Specificity, percentageb |
---|---|---|---|---|---|
mRSSc | 9.0 (11.3) | 7.2 (7.4) | 0.017 | NA | NA |
Digital ulcersd | 19 (65.5) | 93 (37.1) | 0.005 | 17 | 94 |
Lung fibrosisd | 16 (55.2) | 82 (32.7) | 0.023 | 16.3 | 92.9 |
Restrictive lung diseased | 18 (62.1) | 81 (32.3) | 0.001 | 18.2 | 94.8 |
DLCO-SBc | 65.7 (18.1) | 73.7 (20.7) | 0.091 | NA | NA |
Mean FVCc | 80.0 (14.1) | 93.6 (19.2) | <0.005 | NA | NA |
PAHd | 2 (6.9) | 58 (23.1) | 0.054 | 3.3 | 87.7 |
Contracturesd | 23 (79.3) | 149 (59.4) | 0.044 | 13.4 | 94.4 |
CK elevationd | 10 (34.5) | 27 (10.8) | 0.002 | 27 | 92.2 |
Muscle atrophyd | 19 (65.5) | 111 (44.2) | 0.032 | 14.6 | 93.3 |
Colon involvementd | 7(24.1) | 112 (44.6) | 0.046 | 5.9 | 86.3 |
Disease activityc | 2.0 (1.2) | 1.5 (1.3) | 0.037 | NA | NA |