Case | 1 | 2 | 3 | 4 | 5 | 6 |
---|---|---|---|---|---|---|
Anti-snRNPs | Sm, U1RNP | Sm, U1RNP | U1RNP | U1RNP | U1RNP | U1RNP |
Race | Afr Am | Afr Am | Afr Am | Afr Am | Caucasian | Caucasian |
Type of skin involvement | No scl | dcSSc | No scl | No scl | dcSSc | dcSSc |
Pitting scars | Y | Y | Y | Y | Â | Y |
ILD | Y | Y | Y | Y | Y | Â |
Raynaud phenomenon | Y | Y | Y | Y | Y | Y |
Pulmonary hypertension | Â | Y | Â | Â | Â | Â |
Esophageal dysmotility | Â | Â | Â | Â | Â | Y |
Flexion contracture | Â | Y | Â | Â | Â | Y |
Acro-osteolysis | Y | Â | Â | Â | Â | P |
SLE overlap/number of ACR criteria | Y 6 | Y 5 | N 2 | Y 5 | N 2 | N 2 |
PM/DM overlap | Elevated CPK | Â | DM | PM | Â | Â |