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Table 1 Clinical characteristics of patients with immunoglobulin G4-related disease (IgG4-RD).

From: Serum BAFF and APRIL levels in patients with IgG4-related disease and their clinical significance

Case

Age

Serum IgG4

(mg/dL)

RF

ANA

Clinical manifestation

Biopsy/IgG4/IgG ratio

1

73

2890

< 6

40

Lymph, Mikulicz's disease

Prostatitis

Prostate/0.60

2

76

2210

< 6

40

Mikulicz's, RPF

Submandibular gland/0.40

3

79

1460

< 6

160

(SS-A)

IN, IP, Küttner's tumor, Lymph, RPF

Submandibular gland/0.73

4

66

1090

30.3

40

AIP, IN, Renal pseudotumor

Kidney/0.70

5

73

592

< 6

320

IN, IP, Lymph, RPF, Sialadenitis

Submandibular gland/0.43

6

62

736

52.0

< 40

Sialadenitis, Lymph

Parotid gland/0.30*

7

77

738

< 6

< 40

Mikulicz's disease

ND.

8

74

389

< 6

< 40

Retro-orbital tumor

Retro-orbital tumor/0.48

9

76

760

< 6

40

AIP, Periureteritis

Ureter/0.38

10

52

383

< 6

< 40

Küttner's tumor

Submandibular gland/0.57

11

70

724

< 6

< 40

Küttner's tumor, Lymph

Submandibular gland/0.40

12

46

675

26.8

80

Mikulicz's disease

Lachrymal gland/0.41

13

37

533

< 6

< 40

Mikulicz's disease

Lachrymal gland/0.50

14

77

655

< 6

80

RPF

ND

15

76

458

< 6

< 40

AIP, RPF

Retroperitoneal/0.70

16

62

315

< 6

40

(SS-A)

AIP, RPF

Pancreas/0.43

17

79

309

ND

< 40

RPF

ND

18

79

1960

65

40

Orbital tumor, Lymph, Lung nodule

Orbital tumor/0.59

  1. AIP, autoimmune pancreatitis; ANA, antinuclear antibody; IN, interstitial nephritis; IP, interstitial pneumonia; Lymph, lymphadenopathy; ND, not determined; RF, rheumatoid factor; RPF, retroperitoneal fibrosis; SS-A, anti-SS-A antibody; *, IgG4-positive plasmacytes > 100/high-power fields.