Investigations | Group 1 PAH | Group 2 At Risk | Group 3 ILD | Group 4 Controls | Pvalue |
---|---|---|---|---|---|
TTE parameters | Â | Â | Â | Â | Â |
   TRV (m/s) | 3.8 ± 0.7 | 2.95 ± 0.3 | 2.54 ± 0.4 | 2.20 ± 0.2 | < 0.0001 |
sPAP (mm Hg) | 65.8 ± 27.3 | 43.8 ± 7.2 | 32.1 ± 5.3 | 26.3 ± 2.6 | < 0.0001 |
RHC results | Â | Â | Â | Â | Â |
   mPAP (mm Hg) | 40.2 ± 12.5 | N/A | N/A | N/A | N/A |
   mRAP (mm Hg) | 10.1 ± 3.3 | N/A | N/A | N/A | N/A |
PVR (Wood units) | 6.2 ± 3.4 | N/A | N/A | N/A | N/A |
PFT | Â | Â | Â | Â | Â |
   FVC (% pred) | 75.5 ± 23.4 | 100.6 ± 19.5 | 68.7 ± 13.2 | 102.8 ± 13.4 | < 0.0001a |
   DLCOcorr (% pred) | 45.6 ± 11.7 | 61.0 ± 15.1 | 48.0 ± 12.7 | 86.8 ± 13.0 | < 0.0001b |
FVC/DLCOcorr | 1.76 ± 0.38 | 1.73 ± 0.46 | 1.46 ± 0.31 | 1.20 ± 0.20 | < 0.0001c |
6MWD (m) | 337 ± 100 | N/A | 458 ± 84 | N/A | N/A |
Log NT-proBNP | 6.72 ± 1.48 | 5.18 ± 1.11 | 4.72 ± 0.57 | 4.12 ± 0.63 | < 0.0001 |
NT-proBNP (pg/ml) | 1818 ± 2367 | 278 ± 243 | 133 ± 87 | 72 ± 38 | < 0.0001d |