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Table 1 Differential diagnosis of idiopathic CD4 lymphocytopenia

From: Idiopathic CD4 lymphocytopenia: a case of missing, wandering or ineffective T cells

Infections

HIV1,2

 

HTLV1, 2

 

Mycobacterial infections

 

EBV, CMV

Malignancies/hematologic conditions

Lymphoma

 

Aplastic anemia

 

Myelodysplastic syndrome

Autoimmune

Systemic lupus erythematosus

 

Sjögren's syndrome

 

Kikuchi disease

Medications

Chemotherapy and immunosuppressants

 

Corticosteroids

Genetic syndromes

XMEN

 

WHIM

 

Unc119 mutation

Various

Sarcoidosis

 

Common variable immunodeficiency

  1. CMV, cytomegalovirus; EBV, Epstein-Barr virus; Unc119, Uncoordinated 119; WHIM, warts, hypogammaglobulinemia, infections, and myelokathexis; XMEN, X-linked magnesium deficiency with Epstein-Barr virus and neoplasia.