Feature | Rheumatology Unit (n= 45) | Angiology Unit (n= 26) | Pvalue |
---|---|---|---|
Sex (female/male ratio) | 43/2 | 22/4 | NS |
Age (years) | 41 (17-73) | 37.5 (16-71) | NS |
RP duration (years) | 3 (0.5-24) | 3 (1-20) | NS |
Subset 1: antibody-positive, NVC-positive | 26 (57.8) | 6 (2.2) | 0.0098 |
Anti-Scl-70 antibody-positive | 5 (19.2) | 0 | Â |
   ACA-positive | 19 (73.1) | 3 (50) |  |
   Anti-RNA polymerase III antibody-positive | 2 (7.7) | 3 (50) |  |
   Megacapillaries only | 21 (80.8) | 3 (50) |  |
   Avascular areas ± megacapillaries | 5 (19.2) | 3 (50) |  |
Subset 2: antibody-positive, NVC-negative | 16 (35.6) | 0 | - |
   AntiScl-70 antibody-positive | 4 (25) | 0 |  |
   ACA-positive | 12 (75) | 0 |  |
   Anti-RNA polymerase III antibody-positive | 0 | 0 |  |
Subset 3: antibody-negative, NVC-positive | 3 (6.7) | 20 (76.9) | 0.0001 |
   Megacapillaries only | 3 (100) | 20 (100) | - |
   Avascular areas ± megacapillaries | 0 | 0 | - |