Figure 1

Classification of patients with antineutrophil cytoplasmic antibody-associated vasculitis according to the EMEA algorithm in this cohort study. AAV, antineutrophil cytoplasmic antibody-associated vasculitis; ACR, American College of Rheumatology; ANCA, antineutrophil cytoplasmic antibody; EGPA, eosinophilic granulomatosis with polyangiitis (Churg–Strauss syndrome); EMEA, European Medicines Agency; GPA, granulomatosis with polyangiitis (Wegener’s granulomatosis); MPA, microscopic polyangiitis; RLV, renal-limited vasculitis; RV, renal vasculitis.