| EGPA | GPA | MPA/RLV | Unclassifiable |
---|---|---|---|---|
(n = 14) | (n = 33) | (n = 78) | (n = 31) | |
BVAS | 16.1 ± 7.7 | 19.9 ± 7.4 | 18.4 ± 7.3 | 12.1 ± 7.6 |
General | 10 (71.4) | 23 (69.7) | 56 (71.8) | 29 (93.6) |
Cutaneousa,b | 10 (71.4) | 3 (9.1) | 16 (20.5) | 10 (32.3) |
Mucous membranes/eyes | 1 (7.1) | 8 (24.2) | 9 (11.5) | 2 (6.5) |
Ear, nose, and throata,b,c | 6 (42.9) | 28 (84.9) | 7 (9.0) | 1 (3.2) |
Chestc | 5 (35.7) | 22 (66.7) | 30 (38.5) | 6 (19.4) |
Cardiovascular | 2 (14.3) | 4 (12.1) | 6 (7.7) | 0 (0) |
Abdominal | 0 (0) | 1 (3.0) | 0 (0) | 1(3.2) |
Renala,b | 2 (14.3) | 21 (63.6) | 71 (91.0) | 15 (48.4) |
Nervous systema,b | 13 (92.9) | 14 (42.4) | 33 (42.3) | 15 (48.4) |