Patient number | Time to diagnosis (mo) | PVAS/ITAS2010/DEI.Tak at diagnosis | Surgical/endovascular intervention(s) | Follow-up (mo) | Status at last follow-up |
---|---|---|---|---|---|
1 | 42 | 1/6/5 | Repair of LV aneurysm (twice), ascending aorta aneurysm repair, AMPLATZER Septal Occluder device (AGA Medical, Golden Valley, MN, USA) insertion, stent insertion within ascending aorta, coil embolisation of right CA aneurysm | 11 | Remission on treatment |
2 | 2 | 10/15/12 | Mitral valvuloplasty and aortic root replacement, subsequent LIMA bypass graft for stenotic left CA | 32 | Remission on treatment |
3 | 4 | 5/16/7 | – | 16 | Relapse on treatment |
4 | 7 | 10/15/9 | – | 36 | Remission on treatment |
5 | 132 | 2/6/2 | – | 24 | Remission off treatment |
6 | 0 | 2/10/6 | Angioplasty of both renal arteries, SMA and external iliac arteries; coil embolisation of a cerebral artery aneurysm | 168 | Deceased |
7 | 120 | 5/9/7 | – | 11 | Deceased |
8 | 17 | 3/8/8 | – | 6 | Remission on treatment |
9 | 18 | 1/6/5 | – | 6 | Remission off treatment |
10 | 0 | 3/10/5 | Angioplasty of the renal arteries (twice) | 26 | Remission on treatment |
11 | 60 | 12/9/12 | Angioplasty of abdominal aorta; required subsequent surgical repair | 14 | Deceased |