Table 1 Patient characteristics

Patients with GPA, n

28

Male/female, n

16/12

Age, yr, mean ± SD (range)

61.8 ± 16.6 (30–81)

Patients with active GPA (BVAS >0), n (%)

11/28 (39 %)

BVAS (of active GPA), mean ± SD

6.8 ± 7.5

Patients with inactive GPA (BVAS = 0), n (%)

17/28 (61 %)

Duration of remission, yr (of inactive GPA), median ± SD

4.08 ± 2.3

Organ system involvement, n (%)

 ENT

23/28 (82 %)

 Lung

15/28 (54 %)

 Kidney

18/28 (64 %)

 Skin

8/28 (29 %)

 Joints

12/28 (43 %)

 NS

8/28 (29 %)

Localized GPA (upper airways and ENT organs only), n (%)

3/28 (11 %)

Generalized GPA, n (%)

25/28 (89 %)

Number of involved organ systems, mean ± SD

4.3 ± 1.2

Number of relapses, mean ± SD (range)

1.1 ± 1.4 (0–5)

Length of time since disease onset, yr, mean ± SD

9.4 ± 7.9

c-ANCA, n (%)

 Positive

22/28 (79 %)

 Negative

3/28 (11 %)

 Not determinable

3/28 (11 %)