From: IgA vasculitis in adults: the performance of the EULAR/PRINTO/PRES classification criteria in adults
Classified as IgAV by | |||
---|---|---|---|
All (N) | EULAR/PRINTO/PRES criteria (N) | ACR criteria (N) | |
IgA vasculitis | 129 | 128 | 112 |
Controls | 221 | 31 | 42 |
Giant cell arteritis | 121 | 0 | 0 |
ANCA-associated vasculitis | 38 | 13 | 11 |
Cryoglobulinaemic vasculitis | 18 | 10 | 14 |
Secondary vasculitis | 11 | 5 | 8 |
Single organ vasculitis | 8 | 0 | 8 |
Behçet syndrome | 7 | 0 | 0 |
Polyarteritis nodosa | 6 | 0 | 0 |
Takayasu arteritis | 2 | 0 | 0 |
Cogan syndrome | 2 | 0 | 0 |
Anti-GBM disease | 1 | 0 | 0 |
Primary angiitis of the central nervous system | 1 | 0 | 0 |
Anti-C1q vasculitis | 1 | 0 | 0 |
Unclassified vasculitis | 5 | 3 | 1 |