Fig. 2

Mean pulmonary arterial systolic pressure by study. Results from Alkotob et al. are divided into (a) patients with pulmonary fibrosis and (b) patients without pulmonary fibrosis. Results from Collins et al are divided into (a) patients with diffuse systemic sclerosis and (b) patients with limited systemic sclerosis. The weighted mean for estimated systolic pulmonary arterial pressure (sPAP) was 22.2 ± 2.9 mmHg at rest and 43.0 ± 4.3 mmHg at peak exercise