Familial Mediterranean fever is no longer a rare disease in Japan

Table 3 Comparisons of clinical features of patients with different FMF phenotypes

	Sure FMF	Probable FMF
	n = 108	n = 84	p
Male/female	51/57	32/52	0.205
Age at onset (years), mean ± SD	30.5 ± 17.4	30.3 ± 16.6	0.939
Fever	108 (100 %)	76 (90.5 %)	0.001
Frequencies of febrile attack (per month), mean ± SD	1.11 ± 0.93	0.98 ± 0.90	0.309
Duration of fever attack (days), mean ± SD	2.2 ± 0.8	6.2 ± 5.5	<0.0001
Abdominal pain	54 (50.0 %)	23 (27.4 %)	0.002
Thoracic pain	33 (30.6 %)	18 (21.4 %)	0.155
Arthritis	53 (49.1 %)	55 (65.5 %)	0.023
Erysipelas-like erythema	15 (13.9 %)	19 (22.6 %)	0.116
AA amyloidosis	6 (5.6 %)	1 (1.2 %)	0.110
Family history of periodic fever	26 (24.1 %)	13 (15.5 %)	0.142
Rheumatic diseases	14 (13.0 %)	12 (14.3 %)	0.790

Values are shown as n (%) unless otherwise indicated. AA amyloid A, FMF familial Mediterranean fever

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