Table 1 Characteristics of 42 patients with immunoglobulin G4-related disease
From: Circulating plasmablasts/plasma cells: a potential biomarker for IgG4-related disease
Characteristics | Data |
|---|---|
Age at evaluation, years, median (IQR) | 55 (41.5–60) |
Male/female ratio | 2.23:1 |
Baseline responder index, median (IQR) | 14.83 (5.99) |
Diagnosis, n (%) | |
Definite | 32 (76.2) |
Probable | 1 (2.4) |
Possible | 9 (21.4) |
Disease duration, months, median (IQR) | 12 (5.75–36) |
Number of organs involved, mean (SD) | 4.33 (1.79) |
Organs involved, n (%) | |
1 | 1 (2.4) |
2 | 3 (7.1) |
3 or more | 38 (90.5) |
Lymph nodes involved, n (%) | 37 (88.1) |
Salivary glands involved, n (%) | 24 (57.1) |
Lacrimal glands involved, n (%) | 24 (57.1) |
Pancreas involved, n (%) | 13 (31.0) |
Lung involved, n (%) | 13 (31.0) |
Prostate involved of male, n (%) | 12 (41.4) |
Paranasal sinus involved, n (%) | 11 (26.2) |
Retroperitoneal organs involved, n (%) | 11 (26.2) |
Bile duct involved, n (%) | 8 (19.0) |
Kidney involved, n (%) | 6 (14.3) |
Skin involved, n (%) | 4 (9.5) |
History of allergy, n (%) | 29 (69.0) |
Elevated serum IgG4 concentration at baseline, n (%) | 41 (97.6) |
Elevated IgE, n (%) | 26/29 (89.7) |
Eosinophilia, n (%) | 16 (38.1) |