| Present study | Inoue et al. [10] | Lin et al. [11] | Campochiaro et al. [22] | Ebbo et al. [23] | Fernández-Codina et al. [24] | Wallace et al. [9] |
---|---|---|---|---|---|---|---|
Reported year | Â | 2015 | 2015 | 2015 | 2012 | 2015 | 2015 |
Number of patients | 334 | 235 | 118 | 41 | 25 | 55 | 125 |
Country | Japan | Japan | China | Italy | France | Spain | USA |
Mean serum IgG level (mg/dl) | 2403 | NA | 2300 | NA | 2550 | NA | 1573d, 1130e |
Mean serum IgG4 level (mg/dl) | 755 | 470a | 1522 | 284a | 720 | 223a,b, 93a,c | 379d, 51e |
Elevation of IgG4 (%) | 95.5 | 88 | 97.5 | 73 | 100 | NA | 51.4 |
Median serum CRP level (mg/dl) | 0.10 | NA | NA | 0.8 | NA | NA | 0.55d, 0.65e |
Mean serum CRP level (mg/dl) | 0.42 | NA | 0.66 | NA | 3.09 | NA | NA |
CRP < 0.5 mg/dl (%) | 79.9 | NA | NA | NA | NA | NA | NA |
CRP < 1.0 mg/dl (%) | 90.2 | NA | NA | NA | 46 | NA | NA |
Elevation of CRP (%) | 27.4 | NA | 44.1 | 63 | 56 | NA | 67d,f, 46e,f |
Single organ involvement (%) | 11.4 | 42 | 4.2 | 58.5 | 12.0 | 52.7 | 38 |