Table 1 Demographics of the longitudinally observed patients, deceased patients and patients lost to follow up (N = 147)
Demographics | Longitudinally observed patients (N = 118) | Lost to follow up (N = 13) | Deceased before re-examination (N = 16) |
|---|---|---|---|
Age at T1, years, mean (SD) | 44 (14) | 48 (16) | 61 (13)a |
Disease duration at T1 years, mean (SD) | 10 (8) | 11 (9) | 11 (7) |
Male gender, N (%) | 28 (24) | 1 (8) | 4 (25) |
Anti-RNP, U/mL, median (IQR) | 92 (19–240) | 91 (33–235) | 90 (4–196) |
Puffy handsb, N (%) | 108 (92) | 12 (92) | 14 (88) |
Arthritisb, N (%) | 92 (78) | 12 (92) | 12(75) |
Myositisb, N (%) | 36 (30) | 3 (23) | 6 (38) |
Pericarditisb, N (%) | 11 (9) | 2 (15) | 6 (38)c |
Sclerodactyly, N (%) | 33 (28) | 6 (46) | 5 (31) |
Plevritisb, N (%) | 14 (12) | 3 (23) | 4 (25) |
Percentage DLCO pred, mean (SD) | 75 (19) | 75 (14) | 66 (16) |
Percentage FVC pred, mean (SD) | 93 (18) | 88 (19) | 88 (24) |
Interstitial lung disease, N (%) | 39 (34) | 4 (50) | 9 (69)d |