Table 1 Baseline characteristics of patients with IgG4-RD (n = 215)
Variable | Value |
|---|---|
Sex (male:female) | 2.2:1 |
Age (years) | 54 (46, 62) |
Diagnosis, n (%) | |
 Definite | 102 (47.4%) |
 Probable | 10 (4.7%) |
 Possible | 103 (47.9%) |
Disease duration (months) | 12 (4, 36) |
IgG4-RD RI | 14 (10, 18) |
Allergy history, n (%) | 115 (53.5%) |
Number of organs involved, n (%) | |
 1 ~ 2 | 78 (36.3%) |
 3 ~ 4 | 101 (47.0%) |
  ≥ 5 | 36 (16.7%) |
Organ involvement, n (%) | |
 Mikulicz’s disease | 138 (64.2%) |
  Dacryoadenitis | 95 (44.2%) |
  Sialoadenitis | 124 (57.7%) |
 Autoimmune pancreatitis | 91 (42.3%) |
 Sclerosing cholangitis | 58 (27.0%) |
 Retroperitoneal fibrosis | 50 (23.3%) |
 Lung disease | 62 (28.8%) |
 Kidney involvement | 19 (8.8%) |
 Lymphadenopathy | 139 (64.7%) |
 Sinusitis | 62 (28.8%) |
 Prostatitis | 30 (14.0%) |
 Skin involvement | 12 (5.6%) |
 Aortitis/periaortitis | 12 (5.6%) |
 Ophthalmic disease (except for dacryoadenitis) | 7 (3.3%) |
 Mediastinal fibrosis | 9 (4.2%) |
 Hepatopathy | 6 (2.8%) |
 Thyroiditis | 2 (0.9%) |
 Central nervous system involvement | 2 (0.9%) |
Laboratory tests at baseline | |
 Eosinophils (%) | 3.2 (1.6, 6.3) |
 ESR (mm/h) | 25 (10, 59.5) |
 CRP (mg/L) | 3.78 (1.15, 10.81) |
 IgG (g/L) | 18.87 (15.13, 24.53) |
 IgG4 (mg/L) | 8960 (3500, 18,600) |
 IgE (kU/L) | 362.5 (132.5, 774) |