Table 1 Clinical features at baseline and during follow up

Vascular involvement

430 (96.0)

10

 Raynaud phenomenon

424 (94.6)

11

 Fingertip ulcer

128 (28.6)

19

 Loss of finger pad

137 (30.6)

20

 Telangiectasia

153 (34.2)

39

Arthritis

121 (27.0)

66

Muscle involvement

44 (9.8)

11

Pulmonary interstitial disease (ILD)^a

358/447 (80.1)

24

Pulmonary arterial hypertension (PAH)

67/359 (18.7)

11

Gastrointestinal involvement

274 (61.2)

38

 Esophagus

243 (54.2)

40

 Gastric

115 (25.7)

20

 Intestinal

67 (15.0)

13

Cardiac involvement

177/397 (44.6)

97/411

 Arrhythmia

16/396 (4.0)

13/412

 LVEF < 50%

1/396 (0.3)

3/411

 Left ventricular diastolic dysfunction

69/396 (17.4)

70/411

 Pericardial effusion

57/396 (14.4)

53/411

 Valvular disease

88/396 (22.2)

70/412

Renal crisis

5 (1.1)

0

Skin Rodnan score

6 (0, 43)

–