Variable | YOFMF (n = 182) | AOFMF (n = 115) | LOFMF (n = 90) | p value | ||
---|---|---|---|---|---|---|
YOFMF vs AOFMF vs LOFMF | YOFMF vs others | Others vs LOFMF | ||||
Frequency of febrile attack (/month)a | 1.0 (0.3–1.0, n = 157) | 1.0 (0.4–1.0, n = 97) | 0.5 (0.4–1.0, n = 74) | 0.90 | 0.66 | 0.66 |
Duration of fever attack (days)a | 2.5 (2–4, n = 165) | 3 (2–4.8, n = 101) | 2.5 (2–5, n = 71) | 0.25 | 0.25 | 0.75 |
Headache | 25/161 (16%) | 18/91 (20%) | 10/65 (15%) | 0.65 | 0.65 | 0.85 |
Thoracic pain | 82/182 (45%) | 38/115 (33%) | 22/90 (24%) | 0.0025 | 0.0015 | 0.0060 |
Abdominal pain | 117/182 (64%) | 64/115 (56%) | 27/90 (30%) | < 0.0001 | 0.0001 | < 0.0001 |
Pericarditis | 3/161 (2%) | 3/91 (3%) | 4/65 (6%) | 0.25 | 0.21 | 0.13 |
Arthritis | 58/182 (32%) | 55/115 (48%) | 56/90 (62%) | < 0.0001 | < 0.0001 | < 0.0001 |
Myalgia | 13/161 (8%) | 16/91 (18%) | 17/65 (26%) | 0.0014 | 0.0012 | 0.0051 |
Erysipelas-like erythema | 18/182 (10%) | 16/115 (14%) | 17/90 (19%) | 0.11 | 0.10 | 0.076 |
Good response to colchicine | 124/126 (98%) | 85/87 (98%) | 69/71 (97%) | 0.84 | 0.70 | 0.64 |
WBC (× 103/μl)a | 10 (7.2–13, n = 126) | 9.1 (7.2–12.5, n = 64) | 9.1 (7.4–12, n = 48) | 0.84 | 0.65 | 0.94 |
CRP (mg/dl)a | 7.1 (4.0–12.7, n = 132) | 7.1 (2.1–11.1, n = 65) | 9.4 (3.4–15, n = 50) | 0.12 | 0.46 | 0.22 |
SAA (μg/ml)a | 85 (206–1246, n = 43) | 423 (55–1100, n = 13) | 300 (105–702, n = 9) | 0.23 | 0.10 | 0.18 |
ESR (mm/h)a | 40 (24–51, n = 39) | 41.5 (15.5–56, n = 10) | 56 (35–90, n = 15) | 0.063 | 0.075 | 0.019 |
IgD (mg/dl)a | 4.2 (1.1–10.9, n = 17) | 1.5 (1.0–2.3, n = 3) | 10 (1.9–18, n = 2) | 0.41 | 0.64 | 0.46 |