Characteristics | SLE (n = 19) | AAV (n = 7) | PM/DM (n = 3) | RA (n = 2) | SSc (n = 1) |
---|---|---|---|---|---|
Demographic characteristics | |||||
Sex, male to female | 5:14 | 1:6 | 1:2 | 0:2 | 0:1 |
Age, years, mean ± SD | 35.6 ± 15.3 | 53.1 ± 13.0 | 57.0 ± 4.4 | 46.5 ± 9.2 | 46.0 |
Duration of CTD, months, median (IQR) | 4(1.0,21.0) | 3(0.3,84.0) | 120(61.5,180.0) | 204(186.0,222.0) | 108.0 |
Diabetes mellitus, n (%) | 3(15.8) | 1(14.3) | 0(0) | 0(0) | 0(0) |
Nephritis, n (%) | 15(78.9) | 4(57.1) | 0(0) | 0(0) | 0(0) |
Interstitial pneumonia, n (%) | 1(5.3) | 3(42.9) | 1(33.3) | 0(0) | 1(100.0) |
Laboratory data | |||||
WBC count (× 109), mean ± SD | 9.5 ± 6.7 | 10.7 ± 6.0 | 12.9 ± 5.6 | 8.8 ± 1.2 | 6.6 |
Lymphocyte count (× 109), mean ± SD | 0.9 ± 1.0 | 0.8 ± 0.7 | 1.1 ± 0.4 | 1.5 ± 1.0 | 0.7 |
Hemoglobin (g/l), mean ± SD | 96.1 ± 26.2 | 87.3 ± 27.5 | 116.7 ± 2.5 | 114.5 ± 3.5 | 109.0 |
Serum albumin (g/l), mean ± SD | 28.1 ± 7.4 | 32.8 ± 3.5 | 27.0 ± 11.3 | 35.5 ± 4.9 | 32.0 |
Elevated serum creatinine, n (%) | 6(31.6) | 6(85.7) | 0(0) | 0(0) | 0(0) |
IgM (g/l), median (IQR) | 0.7(0.3,0.9) | 0.5(0.4,0.8) | 1.2(1.1,1.4) | 0.7(0,0.5) | 0.3 |
IgG (g/l), median (IQR) | 15.4(7.4,17.4) | 13.4(12.6,20.4) | 15.2(14.4,16.0) | 14.8(0,11.8) | 14.1 |
ESR (mm/h),median (IQR) | 45.0(39,58.5) | 63.0(60,66.0) | 87.5(81.8,93.3) | 49.5(43.3,55.8) | 30.0 |
CRP (mg/l), median (IQR) | 11.0(6.2,33.4) | 12.3(6.3,20.1) | 102.0(52.7,139.0) | 65.6(34.4,96.8) | 0.6 |
Treatment prior to IM | |||||
Median-to-high dose of GC, n (%) | 6(31.6) | 3(42.9) | 2(66.7) | 0(0) | 0(0) |
CYC, n (%) | 4(21.1) | 4(57.1) | 1(33.3) | 0(0) | 0(0) |
MMF, n (%) | 3(15.8) | 0(0) | 0(0) | 0(0) | 0(0) |
CsA, n (%) | 2(10.5) | 0(0) | 0(0) | 1(50.0) | 0(0) |
MTX, n (%) | 1(5.3) | 0(0) | 0(0) | 1(50.0) | 0(0) |