Skip to main content

Table 1 British Isles Lupus Assessment Group Index-2004 (BILAG-2004) for thirty-one patients with childhood-onset SLE (cSLE)

From: Higher interferon score and normal complement levels may identify a distinct clinical subset in children with systemic lupus erythematosus

Total, n = 31

A, n (%)

B, n (%)

C, n (%)

D, n (%)

E, n (%)

Constitutional

2 (6.4)

1 (3.2)

2 (6.4)

22 (71.0)

4 (13.0)

Mucocutaneous

1 (3.2)

5 (16.0)

4 (13.0)

20 (64.5)

1 (3.2)

Neuropsychiatric

1 (3.2)

4 (13.0)

0

8 (25.8)

18 (58.0)

Musculoskeletal

0

4 (13.0)

2 (6.4)

13 (42.0)

12 (38.7)

Cardiorespiratory

2 (6.4)

0

3 (9.7)

9 (29.0)

17 (54.8)

Gastrointestinal

1 (3.2)

0

0

4 (13)

26 (83.9)

Ophthalmic

0

0

0

1 (3.2)

30 (96.8)

Renal

6 (19.3)

5 (16.0)

5 (16.0)

11 (35.5)

4 (13.0)

Haematologic

4 (13.0)

3 (9.7)

8 (25.8)

8 (25.8)

8 (25.8)

  1. Grade A: very active disease requiring immunosuppressive drugs and/or more than 20 mg of prednisolone or equivalent daily; grade B: moderately active disease requiring lower doses of glucocorticoids, antimalarials or nonsteroidal anti-inflammatory drugs (NSAID); grade C: mild stable disease; grade D: no current disease activity but the system had previously been affected; grade E: no current or previous disease activity