Skip to main content

Table 1 British Isles Lupus Assessment Group Index-2004 (BILAG-2004) for thirty-one patients with childhood-onset SLE (cSLE)

From: Higher interferon score and normal complement levels may identify a distinct clinical subset in children with systemic lupus erythematosus

Total, n = 31 A, n (%) B, n (%) C, n (%) D, n (%) E, n (%)
Constitutional 2 (6.4) 1 (3.2) 2 (6.4) 22 (71.0) 4 (13.0)
Mucocutaneous 1 (3.2) 5 (16.0) 4 (13.0) 20 (64.5) 1 (3.2)
Neuropsychiatric 1 (3.2) 4 (13.0) 0 8 (25.8) 18 (58.0)
Musculoskeletal 0 4 (13.0) 2 (6.4) 13 (42.0) 12 (38.7)
Cardiorespiratory 2 (6.4) 0 3 (9.7) 9 (29.0) 17 (54.8)
Gastrointestinal 1 (3.2) 0 0 4 (13) 26 (83.9)
Ophthalmic 0 0 0 1 (3.2) 30 (96.8)
Renal 6 (19.3) 5 (16.0) 5 (16.0) 11 (35.5) 4 (13.0)
Haematologic 4 (13.0) 3 (9.7) 8 (25.8) 8 (25.8) 8 (25.8)
  1. Grade A: very active disease requiring immunosuppressive drugs and/or more than 20 mg of prednisolone or equivalent daily; grade B: moderately active disease requiring lower doses of glucocorticoids, antimalarials or nonsteroidal anti-inflammatory drugs (NSAID); grade C: mild stable disease; grade D: no current disease activity but the system had previously been affected; grade E: no current or previous disease activity