Numbers of patients | 98 |
Male/female | 8/90 |
Median age, years (range) | 58 (21–84) |
Median disease duration, years (range) | 6 (0–26) |
lcSSc/dcSSc | 48/50 |
Autoantibodies | |
ACA, n (%) | 42 (42.8) |
Anti-topoisomerase I, n (%) | 50 (51) |
Others, n (%) | 6 (6.1) |
NVC patterns | |
Early, n (%) | 16 (16.2) |
Active, n (%) | 42 (42.8) |
Late, n (%) | 40 (41) |
Patients on prostanoid therapy, n (%) | 36 (36.7) |
Patients on bosentan/sildenafil therapy, n (%) | 11 (11.2) |