Table 1 Patient characteristics
Demographics | |
Number | 57 |
Age (y) | 34 (26–47) |
Female | 48/9 |
Disease duration (months) | 3 (1–12) |
Clinical features | |
Fever > 39 °C | 46 (80.7) |
Skin rash | 52 (91.2) |
Arthralgia | 52 (91.2) |
Sore throat | 44 (77.2) |
Lymphadenopathy | 43 (75.4) |
Splenomegaly | 25 (43.9) |
Hepatomegaly | 9 (15.8) |
Pleuritis | 20 (35.1) |
Pericarditis | 14 (24.6) |
Weight loss | 14 (24.6) |
Lung disease | 1 (1.8) |
Laboratory findings | |
Leukocytosis (> 10,000/mm3) | 34 (59.7) |
Neutrophils (> 80%) | 36 (63.2) |
Hb < 90 g/L | 9 (15.8) |
PLT < 100,000/mm3 | 2 (3.5) |
ESR > 40 mm/h | 42 (73.7) |
CRP > ULN | 54 (94.7) |
Serum ferritin > 5 ULN | 36 (63.2) |
Abnormal liver function | 36 (63.2) |
Negative ANA (titer ≤ 1:80) | 54 (94.7) |
Negative RF | 56 (98.2) |
IL2R > ULN | 33/45 (73.3) |
Pouchot score | 7 (5–7.5) |