Study/year | Country | Number of subjects with CTD (men/women) | Age of subjects (years; mean ± SD) | CTD | Diagnosis method of ILD | NOS score | |||
---|---|---|---|---|---|---|---|---|---|
Total | CPFE | ILD without emphysema | CPFE | ILD without emphysema | |||||
Antoniou et al./2016 [3] | UK | 333 (74/259) | 41 (18/23) | 292 (56/236) | 53.1 ± 15.1 | 54.4 ± 12.8 | SSc | HRCT | 8 |
Ariani et al./2019 [4] | Italy | 239 (52/187) | 43 (16/27) | 196 (36/160) | 57.7 ± 14.3 | 59.4 ± 13.49 | SSc | CT | 3 |
Champtiaux et al./2018 [5] | France | 108 (40/68) | 36 (27/9) | 72 (13/59) | 48.75 ± 17.02 | 46.75 ± 17.6 | SSc | HRCT | 8 |
Cottin et al./2011 [6] | France | 68 (33/35) | 34 (23/11) | 34 (10/24) | 57 ± 11 | 65 ± 10 | RA 18 (53%) SSc 10 (29%) MCTD 2 (6%) Overlapping CTD 2 (6%) Sjogren’s syndrome 1 (3%) Polymyositis 1 (3%) | HRCT | 8 |
Jacob et al./2018 [7] | South Korea and UK | 245 (110/135) | 129 (85/44) | 116 (25/91) | 63 (median) | 62 (median) | RA | CT | 8 |
Yamakawa et al./2018 [8] | Japan | 21 (3/18) | 16 (2/14) | 5 (1/4) | 60.5 ± 10.5 | 59.8 ± 11.7 | SSc | HRCT | 8 |
Total | – | 1014 (312/702) | 299 (171/128) | 715 (141/574) | – | – | – | HRCT | 8 |