Mean age ± standard deviation (years) | 58 ± 11 |
Sex (F/M) | 16/2 |
Mean Disease duration (years) | 9.7 ± 6.9 |
Anti-Scl70 (n = %) | 10 (55.5%) |
CENP-A and CENP-B (n = %) | 8 (44.5%) |
ILD at CTscan (Yes/No) | 11 (61.1%) / 7 (38.9%) |
Skin involvement (lcSSc / dcSSc) | 14 (77.7%) / 4 (22.3%) |
NVC patterns (E/A/L) | 2 (11.1%) / 10 (55.5%) / 6 (33.4%) |
Therapy | No immunosuppressor = 7 (38.9%) |
MMF = 7 (38.9%) | |
MTX = 2 (11.1%) | |
Cyclosporine = 2 (11.1%) | |
Endothelin receptor antagonists = 8 (44.4%) |