Canada 2002 [23] | USA 2012 [24] | France 2015 [25] | UK 2016 [10] | Germany 2015 [26] | Eurofever 2017 [27] | Germany NPRD 2020 | |
---|---|---|---|---|---|---|---|
Number of Patients | 23 | 70 | 178 | 41 | 95 | 486 | 774 |
Male % | 17 | 33 | 31 | 25 | 42 | 36 | 37 |
Female % | 83 | 67 | 69 | 75 | 56 | 64 | 63 |
Mean of age at disease onset | 9 | 9.7 | 10.9 | 9 | 11.7 | 9.9 | 11.1 |
Delay of diagnosis in months | 13 | 6 | 17 | 15 | 11 | 12 | 8.4 |
Number of lesions mean | 4 | 3.5 | 3 | N/A | 4 | 4 | 3 |
Unifocal in % | 43 | 29 | 7 | 24 | 16 | 29 | 37 |
Multifocal in % | 57 | 71 | 93 | 76 | 84 | 71 | 63 |
Active disease in % after follow-up | 22 | 39 | 66 | N/A | 33 | 50 | 47 |
Months of follow-up | 68 | 22 | 48 | N/A | 49 | N/A | 12 |