From: Latent class analysis of 216 patients with adult-onset Still’s disease
Total (n=216) | Relapse (n=76) | Non-relapse (n=140) | |
---|---|---|---|
General characteristics | |||
Age, median years [IQR] | 51.6 [33.1–68.1] | 50.3 [30.2–65.9] | 47.9 [31.8–69.9] |
Female, n (%) | 164 (75.9%) | 68 (89.4%) | 59 (65.6%) |
Follow-up time, median months [IQR] | 36.8 [12.1–88.2] | 80.6 [40.0–135.8] | 18.8 [8–46.8] |
Proportion of patients with the specific symptom | |||
Fever, % | 99.5% | 100.0% | 98.9% |
Rash, % | 90.7% | 97.3% | 87.1% |
Abnormal liver function tests, % | 81.0% | 85.5% | 76.9% |
Arthralgia, % | 79.5% | 82.6% | 77.8% |
Sore throat, % | 63.3% | 56.1% | 67.1% |
Lymphadenopathy, % | 63.5% | 60.0% | 65.9% |
Splenomegaly, % | 49.5% | 47.8% | 50.4% |
Chest pain, % | 1.9% | 1.3% | 2.1% |
Abdominal pain, % | 1.9% | 1.3% | 2.1% |
Laboratory tests | |||
White blood cell count, median /μL [IQR] | 12600 [9400–18100] | 12600 [9190–17975] | 12630 [9575–18100] |
Neutrophil count, median /μL [IQR] | 10677 [7555–15794] | 10583 [7235–16194] | 10677 [7665–14960] |
Hemoglobin, median g/dL [IQR] | 11.1 [10.1–12.4] | 10.8 [9.8–11.7] | 11.3 [10.2–12.7] |
Platelet, median /μL [IQR] | 258 [163–366] | 260 [170–351] | 256 [159–377] |
Erythrocyte sedimentation rate, median mm/h [IQR] | 76 [41–94] | 80 [40–95] | 75 [44–92] |
Serum aspartate aminotransferase, median U/L [IQR] | 69 [46–128] | 68 [47–125] | 69 [45–130] |
Serum alanine aminotransferase, median U/L [IQR] | 52 [30–104] | 50 [25–87] | 53 [31–110] |
Serum lactate dehydrogenase, median U/L [IQR] | 521 [314–761] | 587 [357–796] | 501 [303–734] |
Serum C-reactive protein, median mg/dL [IQR] | 10.8 [5.7–16.6] | 11 [5.8–18.6] | 10.8 [5.7–14.8] |
Serum ferritin, median ng/mL [IQR] | 7230 [2002–22065] | 8536 [1745–29940] | 6190 [2201–18472] |
Complications | |||
Macrophage activation syndrome, % | 22.3% | 18.4% | 24.5% |
Disseminated intravascular coagulation, % | 13.4% | 17.1% | 11.5% |
Renal dysfunction, % | 3.7% | 3.9% | 3.6% |
Pleuritis, % | 12.5% | 10.7% | 13.6% |
Pericarditis, % | 7.4% | 4.0% | 9.3% |
Myocarditis, % | 0.0% | 0.0% | 0.0% |
Interstitial pneumonia, % | 2.3% | 2.7% | 2.1% |