| Total AAV | Newly diagnosed AAV | Relapsed AAV | ||||||
---|---|---|---|---|---|---|---|---|---|
HP (n = 30) | Non-HP (n = 633) | p-values | HP (n = 20) | Non-HP (n = 538) | p-values | HP (n = 10) | Non-HP (n = 95) | p-values | |
Nervous system, number (%) | |||||||||
 Headache | 21 (70) | 34 (5.7) | < 0.0001 | 16 (80) | 29 (5.4) | < 0.0001 | 5 (50) | 10 (11) | 0.005 |
 Meningitis | 3 (10) | 2 (0.3) | 0.0007 | 1 (5) | 1 (0.2) | 0.071 | 2 (20) | 1 (1.1) | 0.023 |
 Organic confusion | 1 (3.3) | 6 (0.9) | 0.278 | 1 (5) | 6 (1.1) | 0.227 | 0 | 0 | – |
 Seizures | 0 | 4 (0.6) | 1 | 0 | 2 (0.3) | 1 | 0 | 2 (2.1) | 0.999 |
 Stroke | 0 | 9 (1.4) | 0.999 | 0 | 8 (1.5) | 0.999 | 0 | 1 (1.1) | 0.999 |
 Spinal cord lesion | 3 (10) | 2 (0.3) | 0.0008 | 1 (5) | 1 (0.2) | 0.007 | 2 (20) | 1 (1.1) | 0.023 |
 Cranial nerve palsy | 10 (33) | 19 (3) | < 0.0001 | 5 (25) | 15 (2.8) | 0.0003 | 5 (50) | 4 (4.2) | 0.003 |
 Sensory peripheral neuropathy | 3 (10) | 166 (26) | 0.052 | 3 (15) | 145 (27) | 0.307 | 0 | 21 (22) | 0.206 |
 Mononeuritis multiplex | 0 | 105 (17) | 0.009 | 0 | 93 (17) | 0.034 | 0 | 12 (13) | 0.599 |