Table 1 Characteristics of the 26 patients with granulomatosis with polyangiitis and 19 with relapsing polychondritis associated with tracheobronchial involvement
GPA (n=26) | RP (n=19) | |
|---|---|---|
Age at diagnosis, years | 31 [25; 57] | 47 [39; 53] |
Age at CT scan, years | 42 [31; 63] | 53 [47; 66] |
Female | 17/26 (65%) | 12/19 (63%) |
Myalgia | 7/26 (27%) | 0/19 (0%) |
Arthralgia | 8/26 (31%) | 12/19 (63%) |
Fever | 4/26 (15%) | 4/19 (21%) |
Weight loss | 8/26 (31%) | 2/19 (11%) |
Skin lesions | 4/26 (15%) | 4/19 (21%) |
Ocular involvement | 6/26 (23%) | 10/19 (53%) |
Scleritis | 3/26 (12%) | 3/19 (16%) |
Episcleritis | 3/26 (12%) | 5/19 (26%) |
Uveitis | 1/26 (4%) | 6/19 (32%) |
Others | 1/26 (4%) | 2/19 (11%) |
Otitis | 11/26 (42%) | 2/19 (11%) |
Auricular chondritis | 0/26 (0%) | 14/19 (74%) |
Ear deformity | 0/26 (0%) | 3/19 (16%) |
Sinusitis | 16/26 (62%) | 1/19 (5%) |
Nasal crusts | 19/26 (73%) | 2/19 (11%) |
Septal perforation | 2/26 (8%) | 0/19 (0%) |
Nasal chondritis | 0/26 (0%) | 14/19 (74%) |
Saddle nose deformity | 1/26 (4%) | 9/19 (47%) |
Pericarditis | 2/26 (8%) | 0/19 (0%) |
Cardiomyopathy | 1/26 (4%) | 0/19 (0%) |
Bloody diarrhea | 0/26 (0%) | 1/19 (5%) |
Abdominal pain | 0/26 (0%) | 1/19 (5%) |
Glomerulonephritis | 5/26 (19%) | 0/19 (0%) |
Central nervous system involvement | 1/26 (4%) | 0/19 (0%) |
Mononeuritis multiplex | 3/26 (12%) | 1/19 (5%) |
Polyneuropathy | 0/26 (0%) | 1/19 (5%) |
Autoantibodiesa | 19/25 (76%) | 0/19 (0%) |
PR3-ANCA | 17/25 (68%) | 0/19 (0%) |
MPO-ANCA | 2/25 (8%) | 0/19 (0%) |