Baseline DNSS visit | HSCT | all dc-SSc controls A | p | dc-SSc+ Scl70+ male controls B | p | |
---|---|---|---|---|---|---|
Patient number (N) | 80 | 1513 | --- | 240 | ||
Patient number valid n (%) | 78 (97.5) | 1241 (82.0) | --- | 218 (90.3) | ||
mRSS (mean ± SD) | 17.7 ± 11.7 | 15.6 ± 9.9 | 0.156 | 17.2 ± 9.7 | 0.860 | |
mRSS < 10 (N (%)) | 25 (32.1) | 423 (34.1) | 0.805 | 59 (27.1) | 0.464 | |
mRSS > 10 | 53 (68.0) | 818 (65.9) | 159 (72.9) | |||
mRSS > 15 | 42 (53.8) | 557 (44.9) | 0.128 | 115 (52.8) | 0.895 | |
mRSS > 20 | 32 (41.0) | 350 (28.2) | 0.020 | 70 (32.1) | 0.167 | |
Lung involvement | PAH only | 0 | 58 ( 3.8) | 0.186 | 9 (3.8) | 0.288 |
ILD only | 42 (52.5) | 658 (43.5) | 113 (47.1) | |||
PAH + ILD | 11 (13.8) | 171 (11.3) | 28 (11.7) | |||
none | 26 (32.5) | 522 (34.5) | 87 (36.3) | |||
DLCO SB valid data (N (%)) | 60 (75.0) | 829 (54.8) | 0.001 | 163 (67.9) | 0.147 | |
DLCO SB (%, mean ± SD) | 53.9 ± 17.9 | 63.2 ± 21.9 | 0.006 | 59.1 ± 21.3 | 0.124 | |
DLCO SB <75% (N (%)) | 53 (88.3) | 633 (76.4) | 129 (79.1) | |||
Heart involvement (N (%)) | 19 (23.8) | 243 (16.1) | 0.131 | 52 (21.7) | 0.756 |