1 | 2 | 3 | 4 | 5 | |||
---|---|---|---|---|---|---|---|
Initial | f/u | Initial | f/u | ||||
Diagnosis | Vasculitis? | SSc | Poly -arthritis | SSc | Sine SSc? | ILD | Sjögren's syndrome |
Race/gender | WF | Mixed F | WF | WF | WF | ||
Anti-RNAP III ELISA (u) | 16 | NA | 99 | 127 | 8 | 15 to 47 | 42 |
Proximal scleroderma | N | Y < 10 mo | N | Y 3 mo | N | N | N |
Sclerodactyly | N | Y < 10 mo | N | Y 2 mo | N | N | N |
Pitting scar | N | N | N | N | N | N | N |
ILD | N | N | N | N | N | Y | N |
Raynaud's phenomenon | N | ? | N | Y 6 mo | Y For 10 y | N | N |
Other | Renal crisis 10 mo | Flex.cont PH | ARF (TMA), DCM |