From: A genetic role for macrophage migration inhibitory factor (MIF) in adult-onset Still's disease
 | This study (n= 100) | Esdaile[21] (n= 58) | Larson[22] (n= 17) | Wouters[23] (n= 45) | Carreño[24] (n= 20) |
---|---|---|---|---|---|
Male/female | 3/7 | 3/4 | 10/7 | 2/3 | 9/11 |
Age, years, range | 15, 70 | 16, 35 | 7, 44 | 16, 65 | 17, 57 |
Positive patients, % | |||||
Fever(temperature ≥39°C) | 99 | 83 | 100 | 84 | 100 |
Rash | 88 | 90 | 84 | 82 | 80 |
Arthritis | 98 | 98 | 100 | 98 | 100 |
Lymphadenopthy | 47 | 45 | 48 | 36 | 50 |
Hepatoasplenomegaly | 41 | 48 | 72 | 71 | 40 |
Hydrohymenitis | 32 | 57 | 48 | 53 | * |