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Table 1 Baseline characteristics of 40 patients with IgG4-related aortitis/periaortitis and periarteritis

From: Clinical course after corticosteroid therapy in IgG4-related aortitis/periaortitis and periarteritis: a retrospective multicenter study

       Location of vascular lesion Luminal dilatation before Tx    Risk factor of arteriosclerosis Initial PSL Tx (mg/day)
  Follow-up IgG IgG4 IgE CRP Extravascular lesions   
Patient (mo) (mg/dl) (mg/dl) (IU/ml) (mg/dl)   Symptoms  
1 204 1,894 128 543 6.2 AA (−) La, Sa abdo P, fever (−) 30
2 120 2,840 693 468 0.1 AA (−) Sa (−) DM, Sm 30
3 96 5,970 3,100 259 1.56 AA (−) La, Sa, Hy, Pa malaise DM, HT 40
4 78 2,140 557 266 <0.10 AA, IA (+) La, Sa (−) DL, Sm 50
5 70 1,500 173 151 0.3 IA, SMA (−) Pa, RF abdo P DM, HT, DL, Sm 20
6 63 2,970 1,330 419 <0.10 AA (−) La, Sa, Pa, Ki, RF malaise DM, HT, DL, Sm 40
7 63 2,130 715 253 <0.10 IA (−) La, Sa (−) DM, DL, Sm 40
8 63 2,731 269 975 0.6 AA (−) Sa, RF (−) DM, HT, DL, Sm 30
9 57 1,790b 105b 212b 1.5b AA, IA (+) Hy, Lu, Pa, Ly (−) DL 40
10 54 2,570 1,420 345 0.3 AA, IA (+) Pa (−) DM, HT 20
11 48 2,950 1,540 7.9 <0.1 AA (−) Sa, Bi, Pa, Pr (−) DM 30
12 43 1,487 196 447 0.6 AA, IA (−) RF abdo P DM, HT, DL, Sm 0
13 37 2,563 1,330 283 0.09 AA (−) Sa, Ki pollakiuria DL, Sm 45
14 35 2,319 734 542 1.19 TA, AA (−) Sa, Pa, Ki (−) DM, DL 40
15 34 1,458 158 452 0.22 AA (−) Sa, Ly (−) DM, HT, DL, Sm 30
16 27 2,081 870 1,285 0.0 AA, IA (−) Sa, RF, Pr (−) DM, HT 20
17 27 1,756 408 513 0.2 AA, IA (−) Sa, Pa, Ki (−) DM, HT, DL, Sm 20
18 27 1,762 144 24 0.32 AA, IA (+) Pa (−) DL, Sm 20
19 25 2,024 292 1,400 0.14 AA (−) Pa, RF (−) DM, HT, Sm 40
20 24 2,262 299 443 <0.05 AA (−) (−) (−) HT 0
21 24 2,184 236 365 0.3 AA (+) La, Sa fever DM, HT, DL 30
22 22 3,484 1,896 247 0.0 AA (−) La, Sa, Pa, Ki, Ly (−) Sm 35
23 15 4,171 2,120 <20 0.32 AA, IA (−) La, Sa, Ki (−) DM, HT, Sm 40
24 13 1,837 261 687 0.06 IA (−) RF (−) HT, DL 30
25 13 1,454 196 350 0.13 AA, IA (−) (−) abdo P Sm 15
26 10 2,213 455 NA 0.56 AA, IA (−) Sa, Ki arthralgia HT, DL, Sm 40
27 10 3,120 1,020 1,760 1.5 AA, IA, IMA (−) La, Sa hoarseness, fever Sm 30
28 9 2,936 1,070 17 0.0 TA, AA, IA (−) La, Sa, Pa, Ki thirst DM, DL, Sm 40
29 9 10,121 2,500 <20 0.37 IA (+) Pa, Ki, Ly malaise DM 50
30 9 1,200 147 NA 2.94 AA, IA (−) (−) fever, malaise DM, HT 30
31 8 1,475 210 111 0.3 IA (−) Sa (−) (−) 40
32 4 2,938 1,520 48 0.1 AA (−) La, Sa, Ki, RF (−) Sm 30
33 4 1,463 672 216 0.13 AA (−) Sa, Pl, Ca (−) Sm 0
34 3 2,439 782 703 0.2 AA, IA (−) La, Ki, RF (−) DM, DL, Sm 20
35 3 2,244 503 311 0.0 AA, IA (−) Ki edema (−) 30
36 2 1,950 711 737 0.0 AA (−) La, Sa, Lu, Ki (−) Sm 35
37 2 1,328 106 19 0.28 AA, IA (+) RF (−) DL 0
38 1 4,420 2,680 174 0.1 IA (−) La, Sa, Bi, Pa, Ki, Ne diarrhea Sm 50
39 1 2,276 835 <20 0.91 IA (−) Sa (−) HT 15
40 1 1,600 206 212 0.38 AA (−) (−) abdo P, malaise Sm 30
  1. AA, Abdominal aorta; abdo, Abdominal; Bi, Bile tract; Ca, Pericarditis; CRP, C-reactive protein; DL, Dyslipidemia; DM, Diabetes mellitus; F, Female; HT, Hypertension; Hy, Hypophysitis; IA, Iliac artery; IgE, Serum immunoglobulin E at diagnosis; IgG, Serum immunoglobulin G at diagnosis; IgG4, Serum immunoglobulin G4 at diagnosis; IMA, Inferior mesenteric artery; Ki, IgG4-related kidney disease; La, Lacrimal gland, Lu, Lung; Ly, Lymph node; M, Male; Mo, month; NA, Not available; Ne, Nerve; P, Pain; Pa, Pancreas; Pl, Pleuritis; Pr, P rostate; PSL, Prednisolone; RF, Retroperitoneal fibrosis; Sa, Salivary gland; Sm, Past or current smoking; SMA, Superior mesenteric artery; TA, Thoracic aorta; Tx, Treatment. bValue under corticosteroid therapy.