Patient characteristics (n = 94) | Data |
---|---|
Male gender, n (%) | 44 (47 %) |
Age, years, median (min-max) | 60 (21–90) |
ANCA type | |
PR3, n (%) | 47 (50 %) |
MPO, n (%) | 37 (39 %) |
Negative, n (%) | 1 (1 %) |
Double-positive for ANCA and anti-GBM, n (%) | 8 (9 %) |
Reason for PLEX | |
Severe renal involvement without AH, n (%) | 49 (52 %) |
AH without severe renal involvement, n (%) | 9 (10 %) |
Both severe renal involvement and AH, n (%) | 33 (35 %) |
Other, n (%) | 3 (3 %) |
Serum creatinine in non-dialysed, median (min-max) | 369 (40–693) |
Patients on dialysis, n (%) | 55 (59 %) |
Active organ involvement | |
Kidney, n (%) | 91 (97 %) |
Lungs, n (%) | 61 (65 %) |
ENT, n (%) | 25 (27 %) |
Eyes, n (%) | 5 (5 %) |
Skin, n (%) | 9 (10 %) |
Peripheral nervous system, n (%) | 7 (7 %) |
Other, n (%) | 3 (3 %) |