PM/DM-ILD (n = 116) | Non-survivore (n = 14) | Survivor (n = 102) | P value | |
---|---|---|---|---|
Women (n (%)) | 8/14 (57.1%) | 75/102 (73.5%) | 0.22 | |
Type (n) | PM 1, DM 8, CADM 5 | PM 21, DM 43, CADM 38 | 0.41 | |
Age (years) | 60.1 ± 9.6b | 55.5 ± 15.4b | 0.14 | |
Baseline data | KL-6 (U/ml) | 935 (809–1230)c | 612 (431–1023)c | 0.016* |
Lymphocyte (/μl) | 714 (398–909)c | 1,013 (730–1425)c | 0.002** | |
Albumin (g/dl) | 3.03 ± 0.54b | 3.46 ± 0.55b | 0.014* | |
PaCO2 (mmHg) | 32.6 (31.2–36.0)c | 37.8 (35.3–40.7)c | 0.005** | |
HRCT | Zone A | 2.0 (1.0–2.0)c | 1.0 (0–1.0)c | <0.001** |
Zone B | 2.0 (1.0–2.8)c | 1.0 (0–1.0)c | 0.001** | |
Zone C | 2.0 (1.0–3.8)c | 1.0 (1.0–2.0)c | 0.069 | |
Zone D | 4.0 (3.0–4.8)c | 3.0 (2.0–4.0)c | 0.021* | |
Zone total | 10.0 (6.5–13.5)c | 6.0 (4.0–8.3)c | 0.004** | |
Treatment (n (%)) | Initial PSL dose (mg/kg/day) | 0.96 ± 0.24b | 0.80 ± 0.31b | 0.061 |
mPSL pulse (n (%)) | 14/14 (100%) | 63/102 (61.8%) | 0.002** | |
IVCY (n (%)) | 11/14 (78.6%) | 37/102 (36.3%) | 0.003** | |
Calcineurin inhibitor | 13/14 (92.9%) | 68/101 (67.3%) | 0.062 | |
Combination therapyd | 10/14 (71.4%) | 30/102 (29.4%) | 0.005** | |
Outcome (n (%)) | Serious infection | 11/14 (78.6%) | 27/102 (26.5%) | <0.001** |