Parameters | dcSSc with no HAQ-DI score at any time N = 4132 | dcSSc with ≥ 1 HAQ-DI score N = 690 | dcSSc with ≥ 2 HAQ-DI scores N = 424 |
---|---|---|---|
Age (years) | |||
Mean (SD) | 52.2 (13.6) | 53.8 (12.9) | 53.1 (12.7) |
IQR | 42.6–62.4 | 45.6–62.6 | 43.9–62.3 |
Age (years) at onset of RP, N | 3953 | 677 | 414 |
Mean (SD) | 43.3 (14.7) | 42.4 (14.4) | 42.5 (14.3) |
IQR | 32.7–54.0 | 32.4–52.0 | 32.1–52.3 |
Female, n (%) | 3214 (77.8%) | 537 (77.8%) | 320 (75.5%) |
Disease duration, n (%) | |||
≤ 18 months | 962 (23.3%) | 60 (8.7%) | 39 (9.2%) |
> 18 months | 3170 (76.7%) | 630 (91.3%) | 385 (90.8%) |
Current digital ulcers, n (%) | |||
Yes | 1493 (36.6%) | 120 (18.3%) | 70 (17.3%) |
No | 2585 (63.4%) | 535 (81.7%) | 335 (82.7%) |
Puffy fingers, n (%) | |||
Yes | 972 (48.7%) | 216 (35.5%) | 148 (39.1%) |
No | 1024 (51.3%) | 392 (64.5%) | 231 (60.9%) |
mRSS, N | 3895 | 656 | 403 |
Mean (SD) | 16.4 (9.9) | 11.7 (9.0) | 11.8 (8.6) |
IQR | 9.0–23.0 | 5.0–17.0 | 5.0–17.0 |
HAQ-DI score | |||
Mean (SD) | NA | 1.0 (0.8) | 1.1 (0.8) |
IQR | NA | 0.4–1.6 | 0.4–1.8 |
Advanced organ involvement, n (%) | |||
None | 3448 (83.7%) | 468 (68.8%) | 295 (69.9%) |
One | 585 (14.2%) | 178 (26.2%) | 108 (25.6%) |
Multiple | 86 (2.1%) | 34 (5.0%) | 19 (4.5%) |
Missing | 13 | 10 | 2 |