Table 1 Demographic and clinical features of the patients

Number of cases, n

434

255

179

Male to female

1.32:1

0.96:1

2.14:1

< 0.001*

AECC score

33.0 ± 14.2

37.0 ± 12.9

27.2 ± 14.0

< 0.001*

AECC score ≥ 20, n (%)

344(79.3)

228(89.4)

116(64.8)

< 0.001*

Age of disease onset (years), mean ± SD

52.9 ± 13.5

51.1 ± 13.2

55.5 ± 13.5

0.001*

Age of disease diagnosis (years), mean ± SD

55.4 ± 12.9

54.4 ± 12.6

56.9 ± 13.4

0.054

History of allergic disease, n (%)

214(49.3)

167(65.5)

47(26.3)

< 0.001*

IgG4-RD RI

11.0 ± 6.2

11.4 ± 6.0

10.2 ± 6.3

0.045*

Number of involved organs, median (IQR)

5(3–6)

6(4–7)

3(2–5)

< 0.001*

 1 organ involved

30(6.9)

4(1.6)

26(14.5)

< 0.001*

 2 organs involved

52(12.0)

11(4.3)

41(22.9)

< 0.001*

 3 organs involved

46(10.6)

20(7.8)

26(14.5)

0.026*

  ≥ 4 organs involved

306(70.5)

220(86.3)

86(48.0)

< 0.001*