Table 1 Frequency of interstitial lung disease in some connective tissue diseases
Disease | ILD prevalence | Comment |
|---|---|---|
Systemic sclerosis | Up to 80% (on imaging) 30–40% (clinical disease) [3] |  + anti-Scl-70 is a risk factor |
Polymyositis/dermatomyositis | Up to 65–78% (imaging and PFTs) [4] | More common with anti-synthetase antibodies |
Rheumatoid arthritis | 1–73% [5] | Rare in seronegative disease |
Systemic lupus erythematosus | 3–9% [6] |  |
Sjogren’s syndrome | 10–20% [7] |  |