Table 1 Neurologic manifestations and neuroimaging findings in patients with GPA-related HCP

Number of patients

26

Neurologic involvement [n (%)]

 CNS involvement

26 (100.0%)

 PNS involvement

4 (15.4%)

 Neurologic involvement as initial manifestation

4 (15.4%)

Neurologic manifestations of CNS involvement [n (%)]

 Headache

26 (100.0%)

 Cranial nerve palsy

16 (61.5%)

Multiple CN involvement

 CN I

0 (0%)

 CN II

7 (26.9%)

 CN III

3 (11.5%)

 CN IV

2 (7.7%)

 CN V

6 (23.1%)

 CN VI

3 (11.5%)

 CN VII

7 (26.9%)

 CN VIII

5 (19.2%)

 CN IX

2 (7.7%)

 CN X

2 (7.7%)

 CN XI

0 (0%)

 CN XII

2 (7.7%)

 Pituitary involvement

4 (15.4%)

 Neuroimaging findings indicating HCP

26 (100.0%)

 Diffuse HCP

22 (84.6%)

Sites of HCP involvement [n (%)]

 Falx

5 (19.2%)

 Convexity

12 (46.2%)

 Tentorium

9 (34.6%)

 Skull base

11 (42.3%)

 Sellar region

2 (7.7%)

 CSF pressure^a[mmH2O], median (IQR)

155 (125, 185)

 CSF protein^b[mg/dL], median (IQR)

49 (34.75, 65.25)

 CSF WBC count^b[leukocytes/mm³], median (IQR)

2 (0, 6.75)